Ahụ ikeỌrịa na ọnọdụ

Kawasaki ọrịa

Kawasaki ọrịa bụ nnọọ obere, karịsịa ná mba anyị. Ya aha ọzọ - ibu cell arteritis. The mbụ ahụ a kọwara na 1967 na Japan, ebe ruo ugbu a, ọrịa bụ ihe ndị ọzọ na-ahụkarị ihe ná mba ndị ọzọ.

Ya etiology bụ ma ọ ghọtara ihe, ma dị echiche gị n'ụlọnga bụ a retrovirus nke na-akpata mbufụt nke ọbara arịa na ahụ mmadụ. Ọ bụ na-akpali na Kawasaki ọrịa na-emetụta tumadi umu n'okpuru 4 afọ ndị ebelatawo dịghịzi usoro, na ọtụtụ ugboro karịa ụmụ nwoke. Na mba anyị nchoputa nke "Kawasaki ọrịa" a na-etinye na-adịkarịghị, banyere B10 ikpe kwa afọ. Otú ọ dị, ọnụ ọgụgụ nwere ike ịbụ elu, n'ihi na ọ bụghị ọ bụla dọkịta ada ada na-aghọta ihe mgbaàmà na-etinye ihe na-arịa.

N'agbanyeghị dịgasị iche iche nke ihe mgbaàmà, na ịchọpụta mkpa bụ ihe ole na ole isi ihe. Kawasaki ọrịa amalite na okpomọkụ na-abawanye, nke nwere ike ẹkenịmde si 5-10 ka 15-20dney. Ọrịa ịzụlite conjunctivitis, nke na-emetụta ma anya. Mgbe izu abụọ nke mmalite akpụkpọ n'ọbụ aka na ọbụ na-anọkwasị, blushes na-amalite bee apụ. Ọ na-eme na Kawasaki ọrịa na-esonyere a ọkụ ọkụ na akụkụ dị iche iche nke ahụ ya, yi a polymorphous agwa. Mgbe mgbe, ọ na-tọrọ, na mgbe ahụ kpamkpam. Ọ bụrụ na ị na-ele na ọnụ na-arịa ọrịa nwa, i nwere ike ịhụ na-akpọ "strawberry" ire aza, na-egbuke egbuke red na agba na ọnụnọ nke obere hemorrhages na-agazu n'agbụ, n'ime nke cheeks. Egbugbere ọnụ nwekwara ịza aza na gbawara. Amalite hyperemia akpịrị, gọzie gị mkpọchi emee. Mgbe mgbe na otu aka na olu Lymph na-amụba, nke na-akpata ihe mgbu na palpation. Site Associated mgbaàmà nke Kawasaki ọrịa na-agụnye isi ọwụwa, malaise, nkwonkwo mgbu, afọ mgbu, Bilie mgbu na vomiting.

The nchoputa nke dọkịta na-ewepụta ma na ndabere nke na-adakarị mgbaàmà, na-eduzi ihe ndị ndidi ule. Ọ bụrụ na ụba etoju nke erythrocyte sedimentation ọnụego, C-reactive protein, antitrypsin, transaminases na parameters na ọrịa ọbara na-ekwu banyere ụkọ ọbara na thrombocytosis, dọkịta ga-adịghị ala azụ na-eme ka a nchoputa nke Kawasaki. The ọrịa e ji ọnụnọ nke protein na mmamịrị na abu.

Nke a dị ize ndụ ọrịa na nwere ike ime ka nsogbu obi, ruo mgbe omume nke obi ọdịda, myocardial infarction na jaundice. Ndidi na nwetụrụ enyo nke Kawasaki we chọpụtara a cardiologist na echocardiography. Na nnukwu ụdị ọrịa, e nwere otu mbufụt nke obi muscle. Ọ bụ ezie na ọnụ ọgụgụ, dị otú ahụ ikpe na-obere. Ma aneurysms nke akwara akwara ọtụtụ amalite na 20% nke ọrịa. Ọ bụrụ na n'oge ọrịa ya ga imebi meninges, nwere ike ịzụlite aseptic meningitis. Dị ka nsogbu na-egosi na nkwonkwo ogbu na nkwonkwo, na-emeri nke gallbladder - hydrocephalus, nsogbu na-agụnye otitis media.

Na ọgwụgwọ nke ọrịa na-isi gbakwasara na nchedo obi usoro na mgbochi nke ọdịda ya ọrụ. Onye ọrịa na-kenyere a ndị na-abụghị steroidal mgbochi mkpali ọgwụ ọjọọ na elu doses, Corticosteroid creams na ointments. Daily maka 5-7 ụbọchị ka a ndidi intravenously ndinọ immunoglobulin na welie ọgụ na gbakee ngwa ngwa nke onye ọrịa. Ndị dị otú ahụ a maara nke ọma ọgwụ ọgwụ dị ka aspirin, bụ ike na-enye aka na-alụso obere ọrịa. Ọ na-agwakọta ọtụtụ Njirimara na na-eji dị ka ihe antipyretic, mgbochi mkpali na ọbara-thinning n'ụlọnga. N'ihe banyere Kawasaki ọrịa, ọ na-eji ọbụna maka ụmụaka n'okpuru 12 afọ. Nso nso a, ọbara thinner heparin ndinọ ọrịa. Karịsịa ọma Kawasaki ọrịa na-emeso site na ọgwụ na ahụ ike oru na Israel, ebe ọrịa wara plasmapheresis usoro - adi-ọcha nke ọbara plasma.

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