Budd-Chiari syndrome

Budd-Chiari syndrome emee ya ruru ka a na-aga n'ihu obliteration (mmechi ma ọ bụ ibelata) na lumen nke akwara agwụ n'ime imeju. Chiari kweere na isi ihe mere - isi mbufụt nke hepatic veins. Ma mgbe e mesịrị ya mata na ụfọdụ, mgbe thrombosis nke hepatic veins na usụhọde vena cava.

The akwụkwọ na-akọwa ihe dị 200 ikpe nke bibie endoflebita na hepatic veins (ọrịa , Budd-Chiari syndrome).

Na mmepe nke thrombophlebitis arantsieva duct, nke empties kpọmkwem n'ime ekpe hepatic akwara, n'ime eriri akwara, na nke a syndrome nwere ike ịzụlite na nwata. The n'ime shei nke hepatic veins ma ọ bụ usụhọde vena Vienna (nso confluence nke imeju) na-eto eto, mgbe ụfọdụ sonyeere egbochi mkpụkọ nke ọbara. All a na-akpata mmechi ma ọ bụ ibelata nke lumen nke akwara, nke, n'aka, na-akpata mmepe nke ọnọdụ na-achọghị na mkpakọ nke imeju mkpụrụ ndụ.

Budd-Chiari syndrome amalite na-na ndị ọzọ pathologies: ajọ neoplasms nke imeju, pancreas, akụrụ, wdg, vaskụla ọrịa generalized okike. Imeju nwekwara ike-eme ka ibelata nke hepatic veins. Chiari syndrome nwere ike ime ka na ụfọdụ orunótu Gunma echinococcosis, actinomycosis, ahụ etuto na na.

Clinically, Budd-Chiari syndrome egosipụta mgbaàmà nke isi ọrịa, ọ na-akpata a n'ihu ngosi nwekwara dabere na oge nke occlusion nke veins. Ọ guzo nkọ na gradual ntoputa nke syndrome.

Nnukwu hepatic akwara occlusion akpata mberede ọdịdị vomiting, ihe mgbu na nri elu quadrant ma ọ bụ epigastrium ruru ka ọzịza nke imeju, nakwa dị ka hyperextension Glisson Capsule, amalite ascites, e nwere otu obere yellowness.

Portal ọbara mgbali amalite n'otu oge n'ihi na nke ngwangwa abawanye na mgbali na hepatic sinusoids na veins.

Ascites ọrịa a abụghị ngwọta na diuretics, ọmụmụ na-ewuli elu ngwa ngwa ọzọ mgbe paracentesis, mgbe ụfọdụ, na-eme ememe na-adaba ọbara-ya, nwere ike ịzụlite hydrothorax. Ọ bụrụ na enyekwara thrombosis na-amalite na usụhọde vena cava, mgbe ahụ, e nwere ozizi na ala na nsọtụ, "Medusa isi", na a ìhè nsogbu na-etinyere ya, ọbara-aga.

Na mmepe nke hepatic akwara occlusion ngụkọta enyekwara mesenteric thrombosis, e nwere ihe mgbu na afọ ọsịsa, akwara ozi nsogbu apụta ruru imeju cell ọjọọ iduga ọnwụ n'ime ụbọchị ole na ole.

Mgbe ụfọdụ, ndị syndrome Budd - Chiari, na ele mmadụ anya n'ihu mmechi nke lumen nke akwara nwere ike ime ka a-adịghị ala ala ọrịa ruo ogologo oge. Dị otú ahụ na ọdịdị nke eruba n'ime oge emee nnochianya mgbasa: dilate elu elu akpụkpọ akwara, portal ọbara mgbali na-egosi, na mgbe ahụ na enyekwara na esophageal varicose veins.

Maka nchoputa bụ oké mkpa nke ọnụnọ belata nsogbu na occlusal imeju veins na n'otu oge na-abawanye nke na portal nsogbu, nke a na-ahụrụ site hepato- na splenomanometrii ụzọ. Mee retrograde rentgenogepatografiya nke iche mmadụ na-ẹkenam n'ime hepatic akwara. Ultrasound nchọpụta nsogbu dabeere kpọmkwem ihe ịrịba ama - Onyonyo a ọbara clot na veins.

Enweghị agba doplerrovskogo ọmụmụ-atụ aro Budd-Chiari syndrome na:

• The ọnụnọ nke asị ibe mgbanwe imeju, e ji mara ndị oké imeju abụba ma ọ bụ fibrosis nke imeju anụ ahụ,

• The picture dịghị hepatic veins, n'ihi na ihe atụ, n'ihi na ọnụnọ ha lumen ikwughachi-mma pụta na lumen,

• a ibelata nke usụhọde vena cava,

• ihe ịrịba ama nke portal ọbara mgbali elu, ma ọ bụrụ na ọrịa na-ruo ogologo oge.