Ahụ ikeỌrịa na ọnọdụ

Rossolimo-Melkersson-Rosenthal syndrome: Mgbaàmà, Ọgwụgwọ

Melkersson-Rosenthal syndrome Ọ na-akpọ a-adịghị ala ala ọrịa, na chi atọ n'ime nke isi ihe mgbaàmà. The daa ọrịa nke aha e nwere dọkịta abụọ aha. Melkersson kọwara abụọ mgbaàmà, na a atọ akara Rosenthal. N'ihi ya, ọrịa aha mgbe ndị dọkịta abụọ.

On Melkersson-Rosenthal syndrome

syndrome bụ polyetiological. Nke dị oké mkpa maka ya mmepe nwere ọtụtụ ihe:

  • na-efe efe anataghi;
  • vasomotor ọrịa na butere n'aka pụrụ ịrịa ha;
  • daa ọrịa nke lymphatic usoro na mpaghara nke isi na olu;
  • adịghị ala ala foci nke odontogenic ọrịa;
  • Sinusitis.

Na ọnụnọ nke Melkersson-Rosenthal syndrome bụ omume neuro-degenerative ya Jenesis. Nlọghachite nke ọrịa bụ n'oge a kara aka. Tumadi si Melkersson-Rosenthal syndrome-emetụta ndị mmadụ n'etiti 25 na 35 afọ. Pụrụ ịkpata ọrịa hypothermia na ịṅụbiga mmanya ókè, nakwa dị ka a ọnụ ọgụgụ nke ọgwụ ọjọọ. Bilateral ndisịn idem bụ nkịtị - 75% niile ikpe. Nnọọ adịkarịghị - kwadoro.

Mgbaàmà nke Melkersson-Rosenthal syndrome

Ọrịa na-egosipụta ọzịza nke egbugbere ọnụ na cheeks. Mgbe ahụ nwayọọ nwayọọ ihu uru. Onye na-aghọ siri ike warara anya, ikwu okwu, akụkụ ọnụ wụsara mmiri mmiri. Na pasent 30 nke ọrịa ịzụlite akọrọ ma ọ bụ mmiri anya. Banyere 20% - enwekwukwa nghọta nke ụda ndị dị otú ahụ ruo n'ókè nke na ọ na-aghọ wetara. Olee ihe ọzọ mara Melkersson-Rosenthal syndrome mgbaàmà? Fọrọ nke nta 80% nke ọrịa na mgbakwunye na ọzịza nke egbugbere ọnụ hụrụ ha ike reddening, asụsụ na-abawanye, ya elu na-aghọ mkpumkpu, bumpy. Ọkara nke ndị ọrịa na-enwe a oké isi ọwụwa, ọdụdọ na-apụta.

Olee ihe ọzọ e ji a daa ọrịa?

Gịnị bụ ihe mgbaàmà nke ọrịa ụbụrụ syndrome ji Rossolimo-Melkersson-Rosenthal? Ná mmalite, ọ dị mkpa iji banyere na Rossolimo - bụ aha nke-atọ dọkịta, onye na 1901 kọwara makroheylit (ọnụ ọrịa, na-amụba ha size) na Nchikota ọdịdị ihu akwara paresis. Mgbe e mesịrị ya mere Melkersson. Ma ebe ọ bụ nkọwa Rossolimo ọrịa ya aha mgbe ụfọdụ na-eji na daa ọrịa nke na aha.

Ọrịa ụbụrụ syndrome ekpughe ebumnobi nyochaa. Ọ nwere ike na-egosipụta dị ka:

  • isi ọwụwa (migraine);
  • ọdịdị ihu asymmetry ;
  • ọdịdị ihu mkpọnwụ nke ọdịdị ihu akwara ;
  • mgbaàmà Bell lagophthalmos;
  • xerophthalmia;
  • hyperacusis;
  • dysarthria;
  • angioneurotic edema nke ihu (na-emekarị na egbugbere ọnụ);
  • fissured asụsụ na macroglossia;
  • dizgevzii na ageusia;
  • granulomatous cheilitis.

Dị ka e kpughere syndrome?

Melkersson-Rosenthal syndrome, nke nwere photos n'isiokwu a nwere ike kpebisiri ike site nchoputa. Na nke a, na-enwe:

  • serological ule;
  • X-ray, ọ bụrụ na e a enyo na syndrome bilitere n'ihi na-efe efe (HIV, syphilis, ọrịa Lyme, sarcoidosis);
  • electromyography;
  • Magnetik resonance Onyonyo nke ụbụrụ;
  • ule Neuropathy.

N'ezie

Olee otú ọrịa Melkersson-Rosenthal? The syndrome-amalite na ọzịza nke anụ. Ọ na-ahụ propagates na onu mucosa. Mmụba na egbugbere ọnụ size: top - ọzọ ala - obere. Ị nwere ike mgbu nke ọdịdị ihu akwara, na ekemende ịzụlite mkpọnwụ.

The ọrịa e ji nnukwu mmalite. Ọkọ-amalite ọtụtụ awa. Na-emekarị na ọ bụ ọtụtụ ihe na n'ụzọ zuru ezu were na egbugbere ọnụ, nke na-ese na-egbuke egbuke red, mgbe ụfọdụ, bluish tint egosi. Gburugburu ọnụ pụrụ etolite cracks. Nsogbu n'obi ekwu okwu, ihe isi ike na-eri.

Olee otú a adịghị ala ala ọrịa nke Melkersson-Rosenthal? The syndrome nwekwara-amalite na ọzịza. Ma, ọ bụ mgbe niile, na-amụba ma ọ bụ mbelata mgbe ụfọdụ. Edema echekwara na niile na ihu na-edeghị ede oghere.

Ọ bụ obere ụdị Melkersson-Rosenthal syndrome, mgbe aza cheeks naanị. Nọmalị, nke a bụ nnọọ otu n'ime ha. Ke n'ime n'akụkụ cheeks n'ụzọ doro anya abanyeworị ezé. Nke a ọnọdụ na-ezo site na okwu ahụ bụ "granulomatous ụzọ." Ọ dịghị ihe ịrịba ama nke mbufụt.

ọgwụgwọ

Olee otú Melkersson-Rosenthal syndrome? Dọkịta na-eji awa ahụ ụzọ ma ọ bụ mgbanwe. Ná mmalite, onye ọrịa na-enyocha ịchọpụta pathologies nke nwere ike ime ka ọrịa. Ịwa ahụ ọgwụgwọ adịghị egbochi nlọghachite, na na-eji ndị ọzọ n'ihi na ịchọ mma na nzube, mgbe anụ ahụ na-excised egbugbere ọnụ.

Mgbe mgbanwe ọgwụgwọ arụpụta ihe kasị mma a pụrụ inweta na a Nchikota corticosteroids, ọgwụ nje na ịba ọgwụ ọjọọ. "Prednisolone" e kenyere na "Oxytetracycline". Tee pyrogenic na desensitizing mmadụ. Mgbe nile nje ọgwụ. Ọ bụrụ na onye ọrịa na-emetụ Staphylococcus, mgbe ahụ, na-emetụta "toxoid".

Ndidi na-enwe Melkersson-Rosenthal syndrome, Amanyere bụ iwu ọgwụ multivitamins, calcium pantothenate, nicotinic acid, vitamin A, ẹkedọhọde na "komplamin" N'ihi na mma ka ọbara na-adụ arọ. na ojiji nke N'ezie - 10 ụbọchị. A ọma họpụtara "Cavintonum", "Tanakan" na "stugeron" ka a site 1 2 ọnwa. Ọrịa atara dị ka "Nerobolum". Nke a bụ ọgwụ na-egbochi ịka nká. Na-ahọpụta dị ka ọgwụ na-akụjụ na sedatives.

Ọgwụgwọ topically

Gịnị ụzọ ndị ọzọ a pụrụ iji merie syndrome Melkersson-Rosenthal? Ọgwụgwọ nwere ike ịbụ Nde. N'otu oge ahụ mere ngwa nke heparin ude. Ha ikpokọta na Dimexidum, na-ahapụ 20 nkeji. The usoro a rụrụ 3 na 4 ugboro kwa ụbọchị. The N'ezie - 3-4 izu.

N'ihi na ala egbugbere ọnụ na-eji elektrofarez heparin. Usoro a rụrụ kwa ụbọchị. Mgbe e ji fizlechenii okwukwo Bernard, a helium-Neon laser na ultrasound.

Ngwa nke Corticosteroid na methyluracyl ointments na-eji mkpali Filiks. ihu nkpuchi na-etinyere maka 20 nkeji, 2 3 ugboro kwa ụbọchị. Ke adianade do, ngwa na-mere si keratoplasty ego.

Tee mgbochi (3-4 ml), na-ekpo ọkụ abụọ na-percent lidocaine, novocaine na trimecaine. Ọgwụ na-mere kwa ụbọchị ma ọ bụla ụbọchị abụọ.

Kpatara Melkersson-Rosenthal syndrome

Ọrịa ngwa ngwa na-aghọ ala ala. Nke a na-ike gosiri na mmadụ na-ahụ anya, nke a na-ekpu na mutilated ọzịza. Megide a ndabere-emekarị nwere ịda mbà n'obi na ọrịa uche. N'ihi na ụba ịnọrọ nke egbugbere ọnụ na a nwoke na-ike Lonely na-elo, okwu distortion na-hụrụ. The cracks na-egosi mgbe ọzịza na nwere ike ime na-emerụ bacteria na-eme ka nje ọrịa. Nke a na-emetụta asụsụ. Mgbe ụfọdụ, ọ na-kpuchie na cracks. Ke adianade do, nke a n'ihe ize ndụ na-abawanye n'ihi mmerụ edematous mucosa ezé, n'ihi na ihe atụ, n'oge Lonely nri.

Ndị na-enwe ọrịa a, ọ na-atụ aro ka na-eri ihe nri siri ike: nke mbụ ọmụmụ, a dịgasị iche iche nke ọka na mmiri ara ehi na ngwaahịa. Nke a dị mfe ọtịta nri na ebelata likelihood nke ọjọọ na-edeghị ede mucosa. Mkpụrụ osisi na akwụkwọ nri na-bara uru, ma ha mkpa ka a ga-ebipụ na obere Mpekere ma tinye salads. Large chunks nke ọ bụla nri dị mma ka Mike na ojiji nke cutlery nri.

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